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Porphyria is a group of inherited disorders involving abnormalities in the production of heme pigments (the base material responsible for hemoglobin (red blood cell pigment), myoglobin (reddish muscle cell pigment), and another group of materials called cytochromes. Porphyrias are characterized by 3 major findings: photodermatitis ( light sensitivity causing rashes ), neuropsychiatric complaints, and visceral complaints (such as abdominal pain or cramping).
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The porphyrias are disorders in which the body produces too much porphyrin and insufficient heme (an iron-containing nonprotein portion of the hemoglobin molecule). Porphyrin is a foundation structure for heme and certain enzymes.
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The porphyrias are disorders in which the body produces too much porphyrin and insufficient heme (an iron-containing non-protein portion of the hemoglobin molecule). Porphyrin is a foundation structure for heme and certain enzymes.
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The porphyrias are disorders in which the body produces too much porphyrin and insufficient heme (an iron-containing nonprotein portion of the hemoglobin molecule). Porphyrin is a foundation structure for heme and certain enzymes.
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The porphyrias are a group of rare disorders that affect heme biosynthesis. Heme is an essential component of hemoglobin as well as of many enzymes throughout the body.
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The porphyrias are disorders in which the body produces too much porphyrin and insufficient heme (an iron-containing non-protein portion of the hemoglobin molecule). Porphyrin is a foundation structure for heme and certain enzymes.
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